Spontaneous rupture of an intratumoral pseudoaneurysm in a giant renal angiomyolipoma

Authors

  • Mawaddah Abdul Malik School of Medicine, KPJ Healthcare University College, 71800, Nilai, Negeri Sembilan, Malaysia
  • Anas Tharek Department of Radiology, Hospital Pengajar Universiti Putra Malaysia, Faculty of Medicine and Health Sciences, Universiti Putra Malaysia, 43400, Sedang, Selangor, Malaysia
  • Faizal Firdaus Kairuddin School of Medicine, KPJ Healthcare University College, 71800, Nilai, Negeri Sembilan, Malaysia
  • Soo Tze Hui Department of Radiology, Hospital Pengajar Universiti Putra Malaysia, Faculty of Medicine and Health Sciences, Universiti Putra Malaysia, 43400, Sedang, Selangor, Malaysia
  • Idris Ibrahim Department of Radiology, Hospital Pengajar Universiti Putra Malaysia, Faculty of Medicine and Health Sciences, Universiti Putra Malaysia, 43400, Sedang, Selangor, Malaysia
  • Mohd Hazeman Zakaria Department of Radiology, Hospital Pengajar Universiti Putra Malaysia, Faculty of Medicine and Health Sciences, Universiti Putra Malaysia, 43400, Sedang, Selangor, Malaysia
  • Mohd Naim Mohd Yaakob Department of Radiology, Hospital Pengajar Universiti Putra Malaysia, Faculty of Medicine and Health Sciences, Universiti Putra Malaysia, 43400, Sedang, Selangor, Malaysia

DOI:

https://doi.org/10.32896/tij.v2n2.1-5

Keywords:

Angiomyolipoma, Intratumoral hemorrhage, Pseudoaneurysm, Tuberous Sclerosis

Abstract

We reported a rare case of a spontaneous rupture of an intratumoral pseudoaneurysm in a giant renal angiomyolipoma of a 52-year-old lady. The initial presentation was a sudden onset of right hypochondriac pain, nausea, and vomiting. CT scan revealed large heterogenous exophytic enhancing mass with mixed solid and fat density within, arising from the right kidney likely represent a giant right renal angiomyolipoma. There is associated right perinephric hematoma and active bleeding within the mass. No features suggestive of tuberous sclerosis. Subsequent right renal angiogram revealed a pseudoaneurysm of an inferior segmental right renal artery and emergency embolization was done with successful obliteration of the aneurysmal sac and devascularization of the mass.

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Published

2022-09-08

How to Cite

Abdul Malik, M., Tharek, A., Kairuddin, F. F., Hui, S. T., Ibrahim, I., Zakaria, M. H., & Mohd Yaakob, M. N. (2022). Spontaneous rupture of an intratumoral pseudoaneurysm in a giant renal angiomyolipoma. The Interventionalist Journal, 2(2), 1–5. https://doi.org/10.32896/tij.v2n2.1-5